Case Report
Familial en Coup de Sabre With Neuropsychiatric Manifestations: A Case Report
1 Department of Dermatology, Venereology and Leprosy, Sri Venkateshwaraa Medical College Hospital and Research Centre, Ariyur, Pondicherry,
2 Department of Pathology, Sri Venkateshwaraa Medical College Hospital and Research Centre, Ariyur, Pondicherry, India
Anahtar Kelimeler: Familial en coup de sabreneuropsychiatric manifestations
Keywords: Familial en coup de sabreneuropsychiatric manifestations
Abstract
ABSTRACT
Observation:
En coup de sabre is a localised collagen vascular disorder which may sometimes be associated with deeper involvement of underlying neurological involvement. It is multifactorial in causation and genetic predisposition has a definite role to play. A classical case of en coup de sabre is described in a 13 year old boy with interesting neuropychiatric associations. The presence of similar lesions in his mother makes the case even more interesting. Though psychiatric associations are less commonly described with en coup de sabre, it should be looked for. The familial occurrence highlights the genetic and probably environmental causation of this disease.