Unilateral Keratosis Lichenoides Chronica

Keratosis lichenoides chronica (KLC) or Nekam´s disease is a rare, chronic and progressive dermatosis. Around 70 cases have been reported in the literature. It is characterized by violaceous hyperkeratotic papules and plaques that are generally symmetrically arranged in a linear or reticular pattern on the trunk and extremities. The lesions are usually bilateral. KLC is chronic, progressive and medically resistant course.

Herein, we report a 27-year old presenting with thick hyperkeratotic plaques, some of them evolved into annular shapes, on a background of violaceous erythema along lines of Blaschko extending from the dorsum of the left foot to the left inguinal region. A plaque of 5 cm in diameter located on left side of his trunk and another plaque of 4 cm in diameter on the left proximal upper extremity. A diagnosis of Nekam's disease was clinically and histologically features. Oral acitretin treatment was started, with partially improved. We report a patient showing KLC unilateral distribution and covering several areas exclusively on the left side of his body.