Case Report
Paraneoplastic Pemphigus Accompanying Nerve Sheath Sarcoma: A Case Report
1 Assistant Professor of Dermatology , Kermanshah University of Medical Sciences
2 Associate Professor of Pathology; Molecular Pathology Research Center, Kermanshah University of Medical Sciences
3 Assistant Professor of Thorasic Surgeon, Kermanshah University of Medical Sciences
Anahtar Kelimeler: Paraneoplastic pemphiguserythrodermanerve sheath sarcoma
Keywords: Paraneoplastic pemphiguserythrodermanerve sheath sarcoma
Abstract
ABSTRACT
Observation:
Paraneoplastic pemphigus is a rare immunobullous disease which is associated with an underlying neoplasm. Herein, a case of paraneoplastic pemphigus induced by nerve sheath sarcoma as a rare underlying neoplasm is presented. Our patient had an unusual clinical course and his neoplasm developed 26 months after mucocutaneous disease. In addition to vesiculobullous, erosive and lichenoid lesions, the patient showed erythroderma, which is a very rare cutaneous manifestation of paraneoplastic pemphigus.